CASE REPORT |
|
Year : 2019 | Volume
: 13
| Issue : 3 | Page : 106-109 |
|
Two nights in one day: A case report of paraganglioma in sickle cell disease and a review of the literature
Okeoghene G Egigba1, Clement Odigie Osime1, Victor Ekanem2, Paul Jibril3
1 Department of Surgery, University of Benin Teaching Hospital, Benin City, Edo State, Nigeria 2 Department of Pathology, University of Benin Teaching Hospital, Benin City, Edo State, Nigeria 3 Department of Pathology, National Hospital, Abuja, Nigeria
Correspondence Address:
Clement Odigie Osime Department of Surgery, University of Benin Teaching Hospital, PMB 1111, Ugbowo, Benin City, Edo State Nigeria
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/phmj.phmj_12_19
|
|
Background: Sickle cell disease (SCD) is a chronic lifelong disease seen typically in Sub-Saharan Africans, the Mediterranean region and parts of Asia. The condition may be associated with other clinical entities.
Aim of Presentation: We present a case of malignant variant of paraganglioma in a 34-year-old SCD patient to highlight the fact that some very rare clinical entities may be found in this category of patients.
Case Report: Miss B.O. was a 34-year-old SCD patient who presented with features of an intra-abdominal mass. Incisional biopsy done from a mass arising from the left adrenal gland confirmed a malignant variant of paraganglioma. Post-exploratory laparotomy, the patient's clinical state deteriorated and she died 25 days after surgery.
Conclusion: Malignant variant of a paraganglioma, a very rare clinical condition, may be found in SCD patients.
|
|
|
|
[FULL TEXT] [PDF]* |
|
 |
|